CORRECT DIAGNOSIS:
Cutaneous Collagenous Vasculopathy
DISCUSSION:
Cutaneous collagenous vasculopathy (CCV) is primary cutaneous microangiopathy, first described in 2000 by Salama and Rosenthal.[1] Thus far, 27 cases have been reported in the literature.[2] The entity presents with widespread telangiectasia that is clinically indistinguishable from generalized essential telangiectasia. Histologically, CCV can be distinguished from generalized essential telangiectasia by the presence of dilated thick-walled vessels with depositions of hyaline collagenous material. CCV appears to affect a wide range of ages, including a case report of a pediatric patient, with no gender predilection.[3,4] It is thought to be underdiagnosed since clinically it looks like general essential telangiectasia. Thus far, no associated sequelae have been reported with CCV.
TREATMENT:
Like many other vascular lesions, successful treatment of CCV lesions has been reported with the pulse-dye laser.[5] Other vascular lasers such as the Q-switch Nd:YAG, intense pule light, and argon could potentially be of benefit as well. In this case, the patient did not pursue treatment.
REFERENCES:
Salama SS, Rosenthal D. Cutaneous collagenous vasculopathy with generalized telangiectasia: an immunohistochemical and ultrastructural study. J Cutan Pathol. 2000 Jan;27(1):40-8.
Toda-Brito H, Resende C, Catorze G, Viana I. Cutaneous collagenous vasculopathy: a rare cause of generalized cutaneous telangiectasia. BMJ Case Rep. Jul 8;2015 epublish.
Salama SS. Cutaneous collagenous vasculopathy: a new case series with clinicopathologic and ultrastructural correlation, literature review, and insight into the pathogenesis. Am J Dermatopathol. 2015 May;37(5):368-75.
Lloyd BM, Pruden SJ 2nd, Lind AC, Berk DR. Cutaneous collagenous vasculopathy: report of the first pediatric case. Pediatr Dermatol. 2011 Sep-Oct;28(5):598-9.
Echeverria B, Sanmartin O, Botella-Estrada R, Vitiello M. Cutaneous collagenous vasculopathy successfully treated with pulsed dye laser. Int J Dermatol. 2012 Nov;51(11):1359-62.
